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Table 1 Characteristics of the cases

From: Swenson-like pull-through for treatment of the rare association between Hirschsprung’s disease and anorectal malformation

Case

Age

ARM Type

Post-Operative (ARM) Symptoms

Diagnostic approach

Treatment

Outcome

1

4 years

Recto-prostatic

• Persistent constipation

• Abdominal distension

• Contrast enema

• Rectal biopsy

• Swenson-like pull-through procedure

Resolution of symptoms with a bowel management program

2

1 year

Recto-bulbar

• Severe abdominal distension

• Constipation

• Enterocolitis

• Contrast enema

• Exploration with multiple biopsies

• Colostomy

• Swenson-like pull-through procedure

Improvement in symptoms with infrequent attacks of enterocolitis which respond to medical treatment

3

2 years

Rectoperineal

• Persistent constipation

• Contrast enema

• Rectal biopsy

• Swenson-like pull-through procedure

Resolution of symptoms without the need for laxatives